Neurometabolic Diseases Lab

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21 Methylene blue upregulates Nrf2/ARE genes and prevents tau-related neurotoxicity. Hum Mol Genet. 2014 Mar 3. doi:10.1093/hmg/ddu080 363
22 PGC-1α overexpression exacerbates β-amyloid and tau deposition in a transgenic mouse model of Alzheimer's disease. FASEB J. 2014 Apr;28(4):1745-55 290
23 Mitochondrial dysfunction and oxidative damage cooperatively fuel axonal degeneration in X-linked adrenoleukodystrophy. Biochimie. 2014 Mar;98:143-9 481
24 Pioglitazone halts axonal degeneration in a mouse model of X-linked adrenoleukodystrophy. Brain. 2013 Aug;136(Pt 8):2432-43. 954
25 Impaired mitochondrial oxidative phosphorylation in the peroxisomal disease X-linked adrenoleukodystrophy. Hum Mol Genet. 2013 Aug 15;22(16):3296-305 1014
26 Glutathione imbalance in patients with X-linked adrenoleukodystrophy. Mol Genet Metab. 2013 Aug;109(4):366-70. 294
27 Histone deacetylase inhibitor upregulates peroxisomal fatty acid oxidation and inhibits apoptotic cell death in abcd1-deficient glial cells. PLoS One. 2013 Jul 26;8(7):e70712 275
28 Functional Genomics Reveals Dysregulation of Cortical Olfactory Receptors in Parkinson Disease: Novel Putative Chemoreceptors in the Human Brain. J Neuropathol Exp Neurol. 2013 June 531
29 Cyclophilin D as a potential target for antioxidants in neurodegeneration: the X-ALD case. Biol Chem. 2013 May 1;394(5):621-9 497
30 Oxidative stress regulates the ubiquitin-proteasome system and immunoproteasome functioning in a mouse model of X-adrenoleukodystrophy. Brain 2013 136: 891-904. 940
31 Dietary intake of green tea polyphenols regulates insulin sensitivity with an increase in AMP-activated protein kinase α content and changes in mitochondrial respiratory complexes. Mol Nutr Food Res. 2013 Mar;57(3):459-70 238
32 Oxidative stress modulates mitochondrial failure and cyclophilin D function in X-linked adrenoleukodystrophy. Brain. 2012 Dec;135(Pt 12):3584-98. 1012
33 Bezafibrate administration improves behavioral deficits and tau pathology in P301S mice. Hum Mol Genet. 2012 Dec 1;21(23):5091-105. 790
34 ATP and noradrenaline activate CREB in astrocytes via noncanonical Ca(2+) and cyclic AMP independent pathways. Glia. 2012 Sep;60(9):1330-44. 634
35 The absence of ABCD2 sensitizes mice to disruptions in lipid metabolism by dietary erucic acid. J Lipid Res. 2012 Jun;53(6):1071-9 566
36 Bezafibrate lowers very long-chain fatty acids in X-linked adrenoleukodystrophy fibroblasts by inhibiting fatty acid elongation. J Inherit Metab Dis (2012) 35:1137–1145. 571
37 Oxidative stress underlying axonal degeneration in adrenoleukodystrophy: A paradigm for multifactorial neurodegenerative diseases? Biochim Biophys Acta. 2012 Sep;1822(9):1475-88. 672
38 JNK/ERK/FAK mediate promigratory actions of basic fibroblast growth factor in astrocytes via CCL2 and COX2. Neurosignals. 2012;20(2):86-102. 585
39 Amyloid Generation and Dysfunctional Immunoproteasome Activation with Disease Progression in Animal Model of Familial Alzheimer's Disease. Brain Pathol. 2012 Sep;22(5):636-653. 562
40 Functional genomic analysis unravels a metabolic-inflammatory interplay in adrenoleukodystrophy. 2012 Mar 1;21(5):1062-77. 926
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